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1.
An. pediatr. (2003. Ed. impr.) ; 82(6): 388-396, jun. 2015. tab, ilus
Artículo en Español | IBECS | ID: ibc-139813

RESUMEN

Introducción: La meningitis recurrente es una patología infrecuente. Los factores predisponentes son alteraciones anatómicas o situaciones de inmunodeficiencia. Presentamos 4 casos en los que, excluida una inmunodeficiencia, el microorganismo responsable orientó al defecto anatómico causante de las recurrencias. Pacientes y métodos: Revisión retrospectiva de 4 casos clínicos con diagnóstico de meningitis bacteriana recurrente. Resultados: Caso 1: niño de 30 meses con hipoacusia unilateral, diagnosticado por resonancia magnética (RM) de malformación de Mondini tras 2 episodios de meningitis por Haemophilus influenzae. Reparación quirúrgica tras tercera recurrencia. Caso 2: niña de 14 años diagnosticada por RM de defecto de lámina cribiforme posterior a 3 episodios de meningitis por Streptococcus pneumoniae. Se coloca válvula de derivación ventrículo-peritoneal. Caso 3: niña con meningitis por Staphylococcus aureus a los 2 y 7 meses. La RM muestra seno dérmico occipital que requiere exéresis. Complicación con abscesos cerebelosos por coexistencia de quiste dermoide. Caso 4: niño con meningitis por Streptococcus bovis a los 9 días y porEnterococcus faecium, Klebsiella pneumoniae y Escherichia coli a los 7 meses, con crecimiento de Citrobacter freundii y E. faecium posteriormente. RM compatible con síndrome de Currarino. Incluye fístula rectal de LCR, que se repara quirúrgicamente. A los 4 pacientes se les habían realizado pruebas de imagen durante los primeros episodios de meningitis, informadas como normales. Conclusiones: En los pacientes con meningitis recurrentes se debe valorar la posibilidad de un defecto anatómico; el microorganismo aislado debe ayudar a localizarlo. Es imprescindible conocer la flora normal de los potenciales focos. El tratamiento definitivo es habitualmente quirúrgico (AU)


Introduction: Recurrent meningitis is a rare disease. Anatomical abnormalities and immunodeficiency states are predisposing factors. Four cases, in which immunodeficiency was excluded, are presented. The causal microorganism led to the detection of the anatomical defect responsible for the recurrences. Patients and methods: Retrospective review of 4 cases with clinical diagnosis of recurrent bacterial meningitis. Results: Case 1: a thirty month-old boy with unilateral hearing loss, diagnosed with Mondini abnormality by magnetic resonance imaging (MRI) after 2 episodes of Haemophilus influenzae meningitis. Surgical repair after third recurrence. Case 2: fourteen year-old girl diagnosed by MRI with cribriform plate defect after 3 episodes of meningitis due toStreptococcus pneumoniae. Ventriculoperitoneal shunt was placed. Case 3: girl with meningitis due to Staphylococcus aureus at 2 and 7 months. MRI shows occipital dermal sinus requiring excision. Complication with cerebellar abscesses because of a coexisting dermoid cyst. Case 4: child with meningitis due to Streptococcus bovis at 9 days andEnterococcus faecium, Klebsiella pneumoniae and Escherichia coli at 7 months, with positive cultures to Citrobacter freundii and E. faecium later on. Spinal MRI led to the diagnosis of Currarino syndrome with CSF fistula, which was surgically repaired. The 4 patients had undergone image studies reported as normal during the first episodes. Conclusions: In patients with recurrent meningitis the possibility of an anatomical defect should be considered. The isolated microorganism should help to locate it. It is essential to know the normal flora of the different anatomical sites. The definitive treatment is usually surgical (AU)


Asunto(s)
Niño , Humanos , Meningitis Bacterianas/genética , Meningitis Bacterianas/metabolismo , Fístula Rectal/complicaciones , Fístula Rectal/metabolismo , Pediatría/educación , Meningitis Bacterianas/complicaciones , Meningitis Bacterianas/diagnóstico , Fístula Rectal/genética , Fístula Rectal/patología , Pediatría/ética , Pediatría/métodos
2.
An Pediatr (Barc) ; 82(6): 388-96, 2015 Jun.
Artículo en Español | MEDLINE | ID: mdl-25446794

RESUMEN

INTRODUCTION: Recurrent meningitis is a rare disease. Anatomical abnormalities and immunodeficiency states are predisposing factors. Four cases, in which immunodeficiency was excluded, are presented. The causal microorganism led to the detection of the anatomical defect responsible for the recurrences. PATIENTS AND METHODS: Retrospective review of 4 cases with clinical diagnosis of recurrent bacterial meningitis. RESULTS: Case 1: a thirty month-old boy with unilateral hearing loss, diagnosed with Mondini abnormality by magnetic resonance imaging (MRI) after 2 episodes of Haemophilus influenzae meningitis. Surgical repair after third recurrence. Case 2: fourteen year-old girl diagnosed by MRI with cribriform plate defect after 3 episodes of meningitis due to Streptococcus pneumoniae. Ventriculoperitoneal shunt was placed. Case 3: girl with meningitis due to Staphylococcus aureus at 2 and 7 months. MRI shows occipital dermal sinus requiring excision. Complication with cerebellar abscesses because of a coexisting dermoid cyst. Case 4: child with meningitis due to Streptococcus bovis at 9 days and Enterococcus faecium, Klebsiella pneumoniae and Escherichia coli at 7 months, with positive cultures to Citrobacter freundii and E. faecium later on. Spinal MRI led to the diagnosis of Currarino syndrome with CSF fistula, which was surgically repaired. The 4 patients had undergone image studies reported as normal during the first episodes. CONCLUSIONS: In patients with recurrent meningitis the possibility of an anatomical defect should be considered. The isolated microorganism should help to locate it. It is essential to know the normal flora of the different anatomical sites. The definitive treatment is usually surgical.


Asunto(s)
Anomalías Congénitas , Meningitis Bacterianas/microbiología , Adolescente , Preescolar , Femenino , Humanos , Lactante , Recién Nacido , Masculino , Meningitis Bacterianas/etiología , Recurrencia , Estudios Retrospectivos
3.
An Otorrinolaringol Ibero Am ; 33(2): 101-21, 2006.
Artículo en Español | MEDLINE | ID: mdl-16749720

RESUMEN

The obstructive sleep apnea syndrome (OSAS) is frequent in infancy and childhood. It is caused by a prolonged upper respiratory airway obstructioon during sleep, and adenotonsillar hypertrophy is the most important cause. OSAS may have an impact on physical and cognitive development, but syntoms in children are subtle and may pass unrecognised. Polysomnography is the gold standard technique for OSAS diagnosis and surgical approach with adenotonsillectomy is the most frequently treatment indicated. Early diagnosis and treatment and adequate follow up are important to prevent physical disturbances secondary to chronic hypoxemia and to avoid cognitive deficits associated with disrupted sleep architecture.


Asunto(s)
Tonsila Faríngea/cirugía , Apnea Obstructiva del Sueño/fisiopatología , Tonsilitis/complicaciones , Tonsilitis/cirugía , Adenoidectomía , Niño , Preescolar , Humanos , Polisomnografía , Apnea Obstructiva del Sueño/diagnóstico , Apnea Obstructiva del Sueño/etiología , Privación de Sueño/diagnóstico , Privación de Sueño/etiología , Sueño REM/fisiología , Tonsilectomía
4.
An. otorrinolaringol. Ibero-Am ; 33(2): 101-121, mar.-abr. 2006. tab
Artículo en Es | IBECS | ID: ibc-045395

RESUMEN

El síndrome de apnea obstructiva del sueño (SAOS) esun problema prevalente en la infancia. Se produce como consecuencia de una obstrucción de la vía áerea superior, siendo su principal causa la hipertrofia adenoamigdalar. Da lugar al desarrollo de alteraciones fisicasy cognitivas, aunque sus manifestaciones clínicas sonsutiles en la niñez. La polisomnografia nocturna es la técnica recomendada para su diagnóstico y el tratamiento de elección es la adenoamigdalectomía.Un diagnóstico y un tratamiento precoz será importantepara prevenir trastornos secundarios a la hipoxemia crónica y déficits cognitivos asociados a la fragmentación del sueño


The obstructive sleep apnea syndrome (OSAS) is frequent in infancy and childhood. lt is caused by a prolonged upper respiratory airway obstructioon during sleep, and adenotonsillar hypertrophy is the most important cause. OSAS may have an impact on physical and cognitive development, but syntoms in children are subtle and may pass unrecognised. Polysomnography is the gold standard technique for OSAS diagnosis and surgical approach with adenotonsillectomy is the most frequently treatment indicated. Early diagnosis and treatment and adequate follow up are important to prevent physical disturbances secondary to chronic hypoxemia and to avoid cognitive deficits associated with disrupted sleep architecture


Asunto(s)
Masculino , Femenino , Niño , Humanos , Apnea Obstructiva del Sueño/complicaciones , Apnea Obstructiva del Sueño/diagnóstico , Apnea Obstructiva del Sueño/psicología , Polisomnografía/métodos , Ronquido/diagnóstico , Hipoxia/diagnóstico , Trastornos de Somnolencia Excesiva/diagnóstico , Hipoventilación/diagnóstico , Hipercapnia/diagnóstico , Tonsilectomía/métodos , España/epidemiología , Ronquido/etiología , Hipoventilación/complicaciones , Apnea Central del Sueño/complicaciones , Apnea Central del Sueño/diagnóstico
5.
An Esp Pediatr ; 36(6): 467-9, 1992 Jun.
Artículo en Español | MEDLINE | ID: mdl-1497229

RESUMEN

Pyriform sinus fistula has recently been described as a new, rare and little known pathology. The process develops as latero-cervical suppurative adenitis or acute suppurative thyroiditis, usually on the left side. Radical surgery is mandatory to avoid recurrence. This congenital malformation must be present in the differential diagnosis of recurrent infectious cervical processes, especially in acute thyroiditis. The only curative treatment is complete exeresis of the fistula after meticulous dissection of the fistulous tract. We present three cases of this pathology. The diagnostic approach and surgical treatment are discussed. The recent literature on this topic is reviewed.


Asunto(s)
Región Branquial/cirugía , Fístula/cirugía , Niño , Femenino , Fístula/complicaciones , Fístula/diagnóstico , Humanos , Masculino , Tiroiditis/diagnóstico , Tiroiditis/etiología
6.
An Otorrinolaringol Ibero Am ; 18(4): 403-8, 1991.
Artículo en Español | MEDLINE | ID: mdl-1897717

RESUMEN

Human infection by Listeria Monocytogenes has been considered a rare disease in adults, usually associated to immunosuppressed patients. Meningitis is the main clinical manifestation. Sepsis, endocarditis, peritonitis and circumscribed abscesses are occasionally found.


Asunto(s)
Listeriosis , Enfermedades Linfáticas/etiología , Anciano , Anciano de 80 o más Años , Antibacterianos/uso terapéutico , Femenino , Humanos , Listeriosis/diagnóstico , Listeriosis/tratamiento farmacológico , Enfermedades Linfáticas/diagnóstico , Cuello
7.
An Otorrinolaringol Ibero Am ; 17(5): 505-12, 1990.
Artículo en Español | MEDLINE | ID: mdl-2288401

RESUMEN

The AA. inform about the case of a young man, 23, with immunodeficiency (positive HIV antibodies) and malignant otitis externa associated. They recall the etiopathogenesis, the diagnosis, the evolution and the treatment of the disease, pointing out that this case is the first one (published in the ENT bibliography) of malignant otitis-external otitis and HIV linked together.


Asunto(s)
Seropositividad para VIH/diagnóstico , Otitis Externa/diagnóstico , Infecciones por Pseudomonas/diagnóstico , Síndrome de Inmunodeficiencia Adquirida/complicaciones , Síndrome de Inmunodeficiencia Adquirida/diagnóstico , Adulto , Ciprofloxacina/uso terapéutico , Quimioterapia Combinada , Gentamicinas/uso terapéutico , Anticuerpos Anti-VIH/sangre , Seropositividad para VIH/complicaciones , Humanos , Masculino , Mandíbula/anomalías , Otitis Externa/tratamiento farmacológico , Infecciones por Pseudomonas/tratamiento farmacológico
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